Bilateral gonadoblastoma/dysgerminoma in a 46 XY individual: case report with hormonal studies.
نویسندگان
چکیده
A case of bilateral gonadoblastoma/dysgerminoma in a 46 XY phenotypical female is presented. Increased circulating beta human chorionic gonadotropin (beta-HCG) and testosterone together with a decreased concentration of follicle stimulating hormone (FSH) reflected the activities of these tumours. The patient is alive and well three years later, after treatment by surgery and cobalt therapy.
منابع مشابه
Gonadoblastoma and dysgerminoma associated with 46,XY pure gonadal dysgenesis--a case report.
Gonadoblastoma and dysgerminoma developed in a 24-year-old phenotypic female patient with 46,XY pure gonadal dysgenesis. This patient presented with primary amenorrhea. Clinical characteristics showed a typical stigmata of gonadal dysgenesis: primary amenorrhea, sexual infantilism, a small uterus and bilateral streak gonads. A 46,XY karyotype was made by lymphocyte culture. The patient was coun...
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متن کاملBilateral gonadoblastomas with a left sided dysgerminoma in a true hermaphrodite (disorder of sexual differentiation) with 46, XY karyotype.
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ورودعنوان ژورنال:
- Journal of clinical pathology
دوره 35 4 شماره
صفحات -
تاریخ انتشار 1982